neimann-pick disease 《英文msh词典》Neimann-Pick Disease ; [入口词] Neimann-Pick Disease ; [主题词] Niemann-Pick Diseases ; [英文释义] A group of diseases marked by autosomal recessive inheritance and accumulation of sphingomyelin in cells of the RETICULOENDOTHELIAL SYSTEM. They are divided into 5 subtypes: A-E. Type A (classic infantile form) is caused by a deficiency of SPHINGOMYELIN PHOSPHODIESTERASE and presents at age 6-12 months with progressive hepatosplenomegaly and neurologic deterioration. Type B (non-neuronopathic form) presents in childhood with hepatosplenomegaly and pulmonary infiltrates. Type C (chronic neuronopathic form) is caused by defective intracellular cholesterol transport and is divided into severe infantile,late infantile,juvenile,and neonatal hepatitis forms. Type D (Nova Scotian Variant) is phenotypically similar to type C. Type E is an adult non-neuronopathic form. (From Menkes,Textbook of Child Neurology,5th ed,pp101-4)
neimann pick disease 《英文msh词典》Neimann Pick Disease ; [入口词] Neimann Pick Disease ; [主题词] Niemann-Pick Diseases ; [英文释义] A group of diseases marked by autosomal recessive inheritance and accumulation of sphingomyelin in cells of the RETICULOENDOTHELIAL SYSTEM. They are divided into 5 subtypes: A-E. Type A (classic infantile form) is caused by a deficiency of SPHINGOMYELIN PHOSPHODIESTERASE and presents at age 6-12 months with progressive hepatosplenomegaly and neurologic deterioration. Type B (non-neuronopathic form) presents in childhood with hepatosplenomegaly and pulmonary infiltrates. Type C (chronic neuronopathic form) is caused by defective intracellular cholesterol transport and is divided into severe infantile,late infantile,juvenile,and neonatal hepatitis forms. Type D (Nova Scotian Variant) is phenotypically similar to type C. Type E is an adult non-neuronopathic form. (From Menkes,Textbook of Child Neurology,5th ed,pp101-4)
Combined with the particular environmental conditions in neimenggu, the paper also discusses the influence of winter and overweight vehicles on traffic safety 结合内蒙交通的特殊情况,本论文还从冬季道路和汽车超载方面研究了他们对交通安全的影响。
The calculation software for relay setting of the west neimenggu power grid is upgraded based on the above fault calculation methods and is consequently qualified for relay setting of high voltage power grid 基于文中提出的故障计算方法,对内蒙古西部电网原继电保护整定计算软件进行了升级。可满足高压电网整定计算的需要。
In this paper, a suit of on-line monitoring system of fouling and slagging is developed to guide and optimize the progress of sootblowing, according to the research object, the 330mw generating unit in daqi power plant in neimenggu autonomous region 本文以内蒙达旗电厂330mw机组为研究对象,开发了一套积灰、结渣在线监测系统来指导和优化吹灰过程。
The ice purified beer, a brand of firm, has covered six provinces and three municipalities ( beijing, shanghai, tianjing, hebei, henan, shanxi, hunan, jiangxu and neimenggu ), honestly enlists the province and city surrogates 公司生产的潞斯特冰纯啤酒,已经渗透到全国六省三市(北京、天津、上海、河北省、河南省、陕西省、湖南省、江苏省、内蒙古自治区),并诚招全国各省、市代理商。
Hoop architectural design consultant inc . also has participated in and taken charge planning and design of many projects'in guangdong, shanghai, zhejiang, jiangshu, tianjin, sichuan, shandong, hunan, hubei, jiangxi, henan, heilongjiang, neimenggu, anhui, etc 在中国广东、上海、浙江、江苏、天津、四川、山东、湖南、湖北、江西、河南、黑龙江、内蒙古、安徽等地参与了多个项目规划及建筑设计工作。
Income difference between areas is mostly influenced by wages and salaries; tax expense, regional factors in one province, family structure, labor culture and family possesses played a great role on income difference in liaoning province and neimenggu municipality . non-agriculture obviously increases income difference . forestry, fishery and stockbreeding increase income difference 辽宁省和内蒙古自治区农村居民的税费支出、省区内区域性因素、家庭结构、劳动力文化程度和家庭拥有的财产情况对收入差距的影响都很大;非农产业扩大收入差距的效应明显;农业中的林业、渔业和牧业收入具有扩大收入差距的作用;辽宁省的工资性收入扩大收入差距的作用明显。
The paper summarized theories to interpret rural residents " income difference and math methods to measure income difference, which laid theory base for further analysis and provided empirical materials, it studied general income difference of rural residents by gini coefficient, theil index, decomposed gini coefficient according to income sources, ten equally separated methods and econometric models, and measured and analyzed income difference and its determinants of rural residents between regions and in liaoning province and neimenggu municipality 本文归纳了中国农村居民收入差距理论和收入差距的数学描述,为进一步分析奠定了理论基础和提供了实证素材。本文选用基尼系数、泰尔指数、按收入来源分解基尼系数、十等分组法和计量经济模型研究了中国农村居民总体收入差距情况,测度并分析了中国农村居民地区间收入差距、辽宁省和内蒙古自治区农村居民的收入差距状况以及影响收入差距的因素。
As many of traffic accidents are associated with the defect in highway designing, the author, by using the investigated materials of the traffic accidents in neimenggu, studies the influence of route line, subgrade, pavement, structure and traffic safety installations to traffic safety from the combination of theory and reality 结合内蒙古交通事故调查资料,本论文主要在路线、路基、路面、构造物和交通工程设施等方面从理论和实际相结合的角度研究了它们对交通安全的影响,人和车因素对交通安全的影响也进行了初步探讨。
The paper analyzed general income differences, income difference between districts and income difference in one province or municiplity; the analysis of income difference in one province or municiplity was based on family micro-data of liaoning province and neimenggu municipality and comparative analysis was conducted between them 本文既分析了中国农村居民总体收入差距、区域间的收入差距,又分析了区域内的收入差距。分析区域内的收入差距使用的是辽宁省和内蒙古的农产微观数据,并对辽宁省和内蒙古的研究结果进行了比较分析。
The model trained successfully can be used to compute the real-time boiler's efficiency and other concerned operating parameters of the 300mw generating unit in mengda power plant in neimenggu autonomous region . the model can analyze the real-time boiler efficiency to some degree . at the same time, it can lead to the advanced methods for optimizing the boiler operation 神经网络训练成功的模型可在线对内蒙古蒙达电厂的300mw机组计算锅炉效率及其它运行中关注的参数,在一定程度上起到锅炉效率实时分析的作用,并为锅炉运行提出优化调节的方法。